enchondromatosis-olliers
A 14-year-old boy presents with progressive shortening of his left leg and multiple palpable bony masses. Radiographs demonstrate multiple lucent lesions with stippled calcification in the metaphyses of the distal femur, proximal tibia, and hand phalanges, predominantly affecting the left side. The epiphyseal plates appear irregular with columns of cartilage extending into the metaphysis. Regarding Ollier disease (enchondromatosis):
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Ollier disease is a non-hereditary disorder of enchondral ossification characterized by multiple enc...
The risk of malignant transformation to chondrosarcoma in Ollier disease is 25-50% over a lifetime, ...
Maffucci syndrome combines multiple enchondromas with soft tissue hemangiomas (spindle cell hemangio...
Prophylactic curettage of all enchondromas is recommended at diagnosis to prevent malignant transfor...
Limb length discrepancy in Ollier disease results from physeal involvement with premature closure or...
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