Congenital or Iatrogenic Z-Deformity
Berg Classification
Critical Must-Knows
- Triad: Forefoot Adduction, Midfoot Abduction, Hindfoot Valgus
- Differentiation: From Clubfoot (Hindfoot Varus) and MA (Hindfoot Neutral)
- Radiographic Signs: Increased Talocalcaneal Angle + Adducted Metatarsals
- Surgical Principle: Lengthen lateral column (Evans) + Shorten/Realign medial column
- Lateral Translation: Of the navicular on the talus (unlike MA)
Clinical Pearls
- "Beware the 'Metatarsus Adductus' that doesn't get better with casting
- "Check the hindfoot! If it's valgus, it's Skewfoot
- "Avoid simple metatarsal osteotomies alone - must address hindfoot
- "Look for the 'Z' shape on weight-bearing X-ray
Diagnostic Trap
Do not confuse Skewfoot with Clubfoot or Metatarsus Adductus.
- Clubfoot: Hindfoot Varus.
- Metatarsus Adductus: Hindfoot Neutral/Valgus (mild).
- Skewfoot: Hindfoot Valgus (Severe) + Forefoot Adduction. "If the heel is in valgus and the toes point in, think SKEW."
Pediatric Foot Deformities: The Matrix
| Condition | Forefoot | Hindfoot | Key Feature |
|---|---|---|---|
| Adducted | Neutral/Slight Valgus | Kidney Bean Shape | |
| Adducted | Valgus (Plantarflexed Talus) | Z-Shape / Serpentine | |
| Adducted | Varus (Equinus) | Small calf, stiff | |
| Abducted (Dorsiflexed) | Valgus (Severe Equinus) | Rocker Bottom |
SKEWSKEW Features
| S | Serpentine Z-shaped foot |
| K | K-wire/Kids Often requires surgery |
| E | Eversion Hindfoot in valgus/eversion |
| W | Weight-bearing Diagnosis made on WB X-rays |
| S | Serpentine Z-shaped foot | E | Eversion Hindfoot in valgus/eversion |
| K | K-wire/Kids Often requires surgery | W | Weight-bearing Diagnosis made on WB X-rays |
Hook:SKEW your diagnosis towards the hindfoot.
MECSurgical Strategy
| M | Moseley Described specific osteotomies |
| E | Evans Lengthening Corrects hindfoot valgus |
| C | Cotton Osteotomy Plantarflexes medial column |
| M | Moseley Described specific osteotomies |
| E | Evans Lengthening Corrects hindfoot valgus |
| C | Cotton Osteotomy Plantarflexes medial column |
Hook:MEC - reconstruct the foot from lateral to medial.
IIIEtiology
| I | Idiopathic Primary congenital defect |
| I | Iatrogenic Improper casting of MA |
| I | Inherited Rare familial cases |
| I | Idiopathic Primary congenital defect |
| I | Iatrogenic Improper casting of MA |
| I | Inherited Rare familial cases |
Hook:The 3 I's of Skewfoot.
Overview/Epidemiology
Skewfoot is a complex, often misunderstood deformity encompassing elements of both flatfoot and metatarsus adductus. The foot assumes a "Z" or serpentine shape.
- Forefoot: Adducted (similar to Metatarsus Adductus).
- Midfoot: Abducted (Lateral translation of navicular).
- Hindfoot: Valgus (Everted).
It is distinct from simple Metatarsus Adductus because the hindfoot valgus is pathologic and rigid, often accompanied by Achilles contracture.
Aetiology:
- Primary (Idiopathic): A true congenital germ plasm defect similar to CVT or Clubfoot. It may represent a form of "Undercorrected Clubfoot variant" or a distinct entity.
- Secondary (Iatrogenic): Classic Exam Scenario. A well-meaning clinician casts a rigid Metatarsus Adductus foot. They apply pressure to the medial forefoot to abduct it, but fail to stabilize the hindfoot. The force is transmitted to the hindfoot, pushing it into severe valgus. The forefoot remains adducted relative to the midfoot, but the midfoot breaks laterally. "The foot buckles in the middle." This highlights the importance of the three-point mold technique in casting.
Historical Perspective: The condition was first clearly described by Peabody and Muro (1933) as "Congenital Metatarsus Varus". Later, McCormick and Blount coined the term "Skewfoot" to describe the offset between the forefoot and hindfoot. The understanding of the iatrogenic cause has significantly influenced modern casting techniques for metatarsus adductus.
Pathophysiology, Anatomy & Biomechanics
Pathophysiology / Pathoanatomy:
- Hindfoot: The calcaneus is in valgus and eversion. The talus is plantarflexed (though not as severe as CVT). The sustentaculum tali may be hypoplastic.
- Talonavicular Joint: The navicular is laterally subluxated on the talus head. This is the crucial difference from Metatarsus Adductus (where navicular is medial/neutral).
- Tarsometatarsal Joint (Lisfranc): The metatarsals are adducted relative to the cuneiforms/cuboid.
- Result: The talus points medial, the midfoot shifts lateral, and the forefoot points medial again. A "Zig-Zag".
Achilles Tendon: Usually shortened (contracted), contributing to the hindfoot valgus (as the calcaneus everts to dorsiflex). This acts as a deforming force.
Biomechanics: The foot is mechanically unstable. The ground reaction force passes medial to the subtalar axis, perpetuating the valgus. During the stance phase of gait, the midfoot collapses further into abduction, while the forefoot adduction forces the foot to roll over the lateral border. This causes:
- Medial Talar Head Prominence: Pressure area.
- Lateral Border Callosity: Due to weight bearing on the base of the 5th metatarsal.
- Inefficient Lever Arm: The triceps surae loses its mechanical advantage.
Classification Systems
Berg Classification
Based on AP weight-bearing radiographs.
- Type I (Simple MA): Adducted metatarsals. Normal talocalcaneal angle. Navicular central.
- Type II (Complex MA): Adducted metatarsals. Normal talocalcaneal angle. Navicular laterally translated.
- Type III (Skewfoot): Adducted metatarsals. Increased talocalcaneal angle (Valgus). Navicular laterally subluxated.
Detailed Differential Diagnosis
| Deformity | Forefoot | Midfoot (Navicular) | Hindfoot (Calcaneus) | Ankle | Key Differentiator |
|---|---|---|---|---|---|
| Metatarsus Adductus | Adducted | Medial / Central | Neutral / Mild Valgus | Normal | Flexible Hindfoot |
| Skewfoot | Adducted | Lateral Subluxation | Valgus (Fixed) | Equinus often present | Z-Deformity |
| Clubfoot (TEV) | Adducted | Medial Dislocation | Varus (Fixed) | Equinus (Rigid) | Hindfoot Varus |
| Congenital Vertical Talus | Abducted | Dorsolateral Dislocation | Valgus (Severe) | Equinus (Rigid) | Rocker Bottom / Vertical Talus |
| Pes Planovalgus | Abducted | Sags Plantar | Valgus | Normal / Equinus | Forefoot Abduction |
Why differentiation matters:
- Treating Skewfoot like MA (casting) causes iatrogenic worsening.
- Treating Skewfoot like Clubfoot (Ponseti) is ineffective because the hindfoot is already valgus (Ponseti corrects varus).
- Treating Skewfoot like CVT (Dobbs) is closer to the mark but the forefoot deformity is opposite.
Clinical Assessment
History:
- Often a child treated for "Metatarsus Adductus" that "didn't get better" or "looks worse".
- Parents report the foot looks "flat" but the toes point "in".
- Pain in older children (sinus tarsi pain from valgus, or lateral border pain/bunionette).
- Difficulty with shoe fitting due to the C-shape/Z-shape.
Physical Examination:
- Inspection:
- Weight-bearing: Serpentine Shape.
- Heel in Valgus (Check from behind).
- Midfoot prominent medially (Talar head).
- Forefoot Adducted.
- Range of Motion:
- Subtalar joint: Often stiff/restricted.
- Ankle: Check for equinus (Silfverskiold test).
- Midfoot: Assessment of rigidity of adduction.
- Callosities: Under the talar head (medial) or base of 5th MT (lateral).
- Shoe Inspection: Look for medial wear on the heel counter and lateral wear on the sole.
Investigations
Plain Radiographs (Weight Bearing AP/Lateral):
- AP View:
- Talocalcaneal Angle (Kite's): Increased (greater than 35-40 degrees) indicates Hindfoot Valgus.
- Talus-1st Metatarsal Angle: Broken. The line through the talus passes medial to the 1st MT.
- Metatarsus Adductus Angle: Increased.
- Lateral View:
- Talar Declination: Increased (Talus points down).
- Calcaneal Pitch: Decreased (Flatfoot).
- Meary's Angle: Broken (in extension/dorsiflexion at TN joint).
CT Scan:
- Useful for surgical planning in adolescents (tarsal coalition exclusion).
- Can characterize the specific deformity of the medial cuneiform.
Management Algorithm

Surgical Technique
Evans Calcaneal Lengthening Osteotomy
Rationale: Lengthening the lateral column pushes the navicular medially (reducing its abduction) and corrects hindfoot valgus.
Technique:
- Lateral incision over the calcaneal neck (1.5cm proximal to CC joint).
- Identify and protect Sural Nerve.
- Perform specific osteotomy (transverse) through anterior calcaneus.
- Distract with laminar spreader.
- Insert Tricortical Iliac Crest Allograft (wedge).
- Fixation: Plates or K-wires not always needed if graft is tight, but usually a plate is used for stability.
(Note: Ensure list items are not directly before closing tag)
Complications
| Complication | Risk Factors | Prevention/Management |
|---|---|---|
| Undercorrection | Addressing only one component (e.g., only forefoot). | Principle: Must address both Hindfoot Valgus and Forefoot Adduction. |
| Lateral Column Overload | Excessive Evans graft size. | Intra-operative sizing. Lateral column should not be longer than medial. |
| Non-union | Graft failure, smoking (parents/adolescent). | Rigid fixation, NWB period. |
| CC Joint Arthritis | Evans osteotomy entering the joint. | Fluoroscopic guidance. Stay 1.5cm proximal to joint. |
| Sural Nerve Injury | Lateral approach. | Identify and retract. |
| Overcorrection (Varus) | Too large an Evans graft. | Careful preoperative planning and intraoperative assessment. |
Postoperative Care
Protocol for Double Osteotomy (Evans + Cotton):
- 0-2 Weeks:
- Splint/Backslab in neutral position.
- Strict Elevation.
- Non-weight bearing.
- 2-6 Weeks:
- Wound check.
- Short leg fiberglass cast.
- Molded to hold hindfoot neutral and forefoot abducted.
- Non-weight bearing.
- 6-8 Weeks:
- Radiographic check for graft union.
- Transition to partial weight bearing if union evident.
- 8-12 Weeks:
- Walking cast or CAM boot.
- Full weight bearing.
- 3-6 Months:
- Transition to shoes with arch support.
- Physiotherapy for ankle and subtalar motion.
Outcomes/Prognosis
- Non-operative: Generally poor for rigid skewfoot. Pain and footwear difficulties persist. The deformity tends to progress with growth.
- Operative: Good functional results with "double osteotomy" techniques (Evans + Medial Column). Mosca (1995) reported excellent results using the Evans procedure for valgus deformities including skewfoot.
- Satisfaction: High patient and parent satisfaction regarding foot shape and shoe fit.
- Function: Most children return to full sports activities.
- Long Term: Risk of early triple arthrodesis if deformity remains uncorrected due to joint incongruity and degenerative changes. Adult skewfoot is notoriously difficult to reconstruct and often requires fusion.
- Recurrence: Can occur if the Evans graft resorbs or if the medial column was under-corrected. Monitoring until skeletal maturity is advised.
Evidence Base
- 31 severe symptomatic valgus hindfoot deformities in 20 children: 25 flatfeet and 6 skewfeet
- Calcaneal (Evans-type) lengthening combined with opening-wedge medial cuneiform osteotomy to correct both hindfoot and forefoot in the skewfeet
- Satisfactory clinical and radiographic correction in all but the 2 most severely deformed feet; subtalar motion preserved
- Resolved pain and plantar-talar-head callus while avoiding arthrodesis
- 16 feet (15 patients) including a 15-year-old skewfoot treated with plantarflexion opening-wedge medial cuneiform osteotomy for fixed forefoot varus
- Talonavicular coverage angle improved a mean of 15 degrees and lateral talo-first metatarsal angle a mean of 14 degrees; no nonunions or malunions
- Preserves first-ray mobility versus first tarsometatarsal arthrodesis, with easily titratable correction
- 8 patients (13 feet) showing that correcting the valgus deformity is as important as addressing the coalition
- Calcaneal lengthening with gastrocnemius/Achilles lengthening relieved pain and preserved talonavicular and calcaneocuboid motion
- Supports treating excessive hindfoot valgus rather than defaulting to triple arthrodesis
Viva Scenarios
Use these scenarios to practise clinical reasoning and management decisions
The Failed Casting
"A 2-year-old child was treated for Metatarsus Adductus with casting. Parents say the foot looks 'flatter and worse'. What happened?"
This is likely iatrogenic skewfoot. The casting likely abducted the forefoot without stabilizing the hindfoot, causing the midfoot to break laterally and the hindfoot to drift into valgus. I would assess this with a weight-bearing radiograph looking for the Z-deformity (high Kite's angle, adducted metatarsals).
Surgical Planning
"8-year-old with painful rigid Skewfoot. Plan surgery."
Conservative management is futile. I would plan for surgical reconstruction addressing both components. 1. Hindfoot Valgus: Evans calcaneal lengthening osteotomy (tricortical graft) to restore lateral column length and realign TN joint. 2. Forefoot Adduction: Medial cuneiform opening wedge osteotomy (Cotton) or metatarsal osteotomies. 3. Soft Tissue: TAL if equinus present.
Differential Diagnosis
"Explain the difference between Clubfoot, Metatarsus Adductus, and Skewfoot to a junior registrar."
It's all about the Hindfoot. In Metatarsus Adductus, the hindfoot is Neutral or Mild Valgus. In Clubfoot, it is Fixed Varus. In Skewfoot, it is Fixed Valgus. The forefoot is adducted in all three (or at least looks it). Skewfoot is effectively a 'Serpentine' foot with a Z-shape.
MCQ Practice Points
Diagnosis MCQ
Q: What is the hallmark radiographic finding in Skewfoot? A: Increased Talocalcaneal Angle (Valgus) + Adducted Metatarsals. This creates the Z-shape.
Etiology MCQ
Q: Which intervention is a known risk factor for iatrogenic skewfoot? A: Serial Casting for Metatarsus Adductus without stabilizing the hindfoot.
Treatment MCQ
Q: The Evans procedure corrects deformities in which plane? A: Triplanar. It corrects valgus (coronal), abduction (transverse), and dorsiflexion (sagittal).
Anatomy MCQ
Q: What is the classic position of the navicular in Skewfoot? A: Dorsolateral subluxation on the talar head. This distinguishes it from MA where the navicular is medial or central.
Classification MCQ
Q: In the Berg classification, which type represents true Skewfoot requiring surgical treatment? A: Type III - rigid forefoot adduction with fixed hindfoot valgus. Type I is simple metatarsus adductus. Type II is complex metatarsus adductus with lateral midfoot shift.
Differential MCQ
Q: What is the key clinical finding that distinguishes Skewfoot from Metatarsus Adductus? A: Fixed hindfoot valgus. In Metatarsus Adductus, the hindfoot is neutral or only mildly valgus. The 'Z-shape' appearance on weight-bearing radiographs confirms Skewfoot.
Controversies & Areas of Uncertainty
Skewfoot has one of the weakest evidence bases in paediatric foot surgery — almost all literature is Level IV/V case series. Examiners reward candidates who can articulate the genuine uncertainty rather than overstate dogma.
- Does the iatrogenic mechanism truly exist? The "failed metatarsus adductus casting" story is widely taught and biomechanically plausible (forefoot abduction levering an unstabilised hindfoot into valgus), but it rests on small series and is hard to separate from a primary congenital deformity that was simply misdiagnosed as metatarsus adductus. Many authors regard most cases as primary.
- Is skewfoot a distinct entity or the severe end of a spectrum? Some authors (including the Tönnis tradition) view "skewfoot" and "serpentine foot" as simply the severe end of complex metatarsus adductus rather than a separate disease, which has implications for how aggressively to treat.
- Single- versus double-osteotomy. Whether every operative skewfoot needs both a lateral-column lengthening and a medial-column procedure, or whether selected feet can be corrected with one, is unresolved; the principle of "address both ends of the Z" is consensus-based, not trial-proven.
- Subtalar arthroereisis. Promoted by some as a less invasive option for the valgus component, but evidence in skewfoot specifically is minimal and complication/implant-removal rates are a concern; most paediatric foot surgeons regard it as adjunctive at best.
- Allograft versus autograft and the role of fixation. Both wedge graft choices have advocates; rigid internal fixation versus reliance on a tightly impacted graft is surgeon-dependent.
- Asymptomatic skewfoot. Because long-term natural history is poorly defined and many feet remain pain-free, the threshold for operating on an asymptomatic deformity is genuinely contested.
Guidelines, Registries & Global Practice
Global epidemiology
- Skewfoot is rare; fewer than ~50 cases were reported in the English literature at the time of Peterson's 1986 series, and most modern data remain single-centre case series.
- No dedicated registry exists for paediatric foot deformities; unlike arthroplasty, there is no NJR/AJRR/AOANJRR equivalent capturing skewfoot outcomes, which is itself a recognised evidence gap.
- Where the deformity follows treatment of metatarsus adductus, true incidence is unknown and almost certainly under-reported.
Society guidance and practice positions (no single-country framing)
| Body / tradition | Position relevant to skewfoot |
|---|---|
| AAOS / POSNA (North America) | No formal clinical practice guideline; teaching follows the Mosca motion-preserving philosophy (calcaneal lengthening plus medial-column osteotomy, avoid early arthrodesis). |
| BOA / BSCOS (UK paediatric tradition) | Emphasis on accurate differentiation from metatarsus adductus and clubfoot, weight-bearing imaging, and reserving surgery for symptomatic rigid deformity. |
| AO Foundation | Reconstruction-principle teaching: correct all components of the deformity, preserve growth and motion, fixation and graft tailored to age. |
| EFORT / European centres (incl. Tönnis tradition) | Often frame severe complex metatarsus adductus and skewfoot as a continuum; selective tendon transfer (e.g. tibialis anterior) and soft-tissue balancing feature in the European literature. |
High- versus limited-resource practice variation
- High-resource settings: weight-bearing radiographs (or simulated weight-bearing/standing CT in adolescents), allograft availability, image intensifier for the calcaneal osteotomy, and access to specialist paediatric orthopaedic foot services.
- Limited-resource settings: reliance on clinical examination and a single plain film; autograft (iliac crest) preferred over allograft for cost and availability; greater use of soft-tissue and simpler single-osteotomy strategies; later presentation of neglected/rigid deformity is more common.
- Universal principles: differentiate the deformity correctly before treating, never cast/brace a foot in a way that drives the hindfoot into valgus, and address both the forefoot adduction and the hindfoot valgus when operating.
SKEWFOOT
Clinical summary
CATCHPHRASE
- •Serpentine Foot
- •Z-Deformity
- •Failed MA Casting
- •The 3 I's: Idiopathic, Iatrogenic, Inherited
- •Rarely resolves spontaneously
TRIAD
- •Hindfoot Valgus
- •Midfoot Abduction
- •Forefoot Adduction
- •Plantarflexed talus
- •Lateral navicular subluxation
RADIOGRAPHS
- •Increased TC Angle (Valgus)
- •Adducted Metatarsals
- •Lateral Navicular
- •Talar head uncoverage
- •Weight-bearing views essential
MANAGEMENT
- •Observe (if flexible)
- •Surgery: Evans + Medial Column Osteotomy
- •Avoid isolated MT osteotomy
- •Must address both ends
- •Casting often fails
KEY TRAP
- •Confusing with Clubfoot (Varus)
- •Confusing with MA (Neutral Hindfoot)
- •Missing the hindfoot valgus
- •Incomplete surgical correction
- •Not using WB X-rays