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Evidence. Clarity. Practice.

© 2026 OrthoVellum. For educational purposes only.

Not medical advice. Verify clinically important information against current local guidance.

Preiser Disease

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Preiser Disease

Comprehensive exam guide to Preiser disease (idiopathic osteonecrosis of the scaphoid): pathophysiology, Herbert-Lanzetta and Kalainov classifications, MRI diagnosis, and stage-based treatment from immobilization to vascularized bone graft and salvage.

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Reviewed: 2026-06-07Maintained by OrthoVellum Medical Education Team
Peer-reviewed editorial processMethodologyReport a correction
High-yield overview

Idiopathic Scaphoid Osteonecrosis | Proximal Pole Disease | Diagnosis of Exclusion

2ndMost common carpal AVN (after lunate)
30-50Typical age (years)
ProximalPole most affected (retrograde supply)
MRIKey diagnostic test

Herbert-Lanzetta Radiographic Staging

Stage I
PatternNormal radiograph; MRI shows AVN
TreatmentImmobilization, observation
Stage II
PatternSclerosis / density change, no fragmentation
TreatmentVascularized graft or radial osteotomy if viable
Stage III
PatternFragmentation / cystic change of proximal pole
TreatmentGraft if no arthritis, else salvage
Stage IV
PatternCollapse with peri-scaphoid (radiocarpal) arthritis
TreatmentSalvage: PRC, four-corner fusion or excision

Critical Must-Knows

  • Diagnosis of exclusion: Preiser is idiopathic AVN with NO acute fracture - rule out occult fracture/nonunion first
  • Retrograde blood supply: dorsal scaphoid branch of the radial artery enters distally, so the PROXIMAL pole is most ischaemic
  • MRI is the key test: diffuse low T1 signal of the scaphoid; Stage I is MRI-only with normal radiographs
  • Kalainov MRI split: complete (entire scaphoid) vs partial (proximal pole only) necrosis - guides graft suitability
  • Salvage when collapsed/arthritic: proximal row carpectomy and four-corner fusion give the most reliable pain relief

Clinical Pearls

  • "
    Scaphoid is the 2nd most common carpal bone for AVN after the lunate
  • "
    Proximal pole disease = retrograde, distally-entering blood supply
  • "
    Normal X-ray does not exclude Preiser - get an MRI
  • "
    No level I evidence and no formal guideline - treatment is staged and individualised

Clinical Imaging

Critical Preiser Disease Exam Points

It Is a Diagnosis of Exclusion

Preiser disease = idiopathic AVN of the scaphoid with NO acute fracture. Before you call it Preiser, exclude an occult fracture or established nonunion (which has its own proximal-pole AVN). The history of insidious pain without significant trauma is the giveaway.

Proximal Pole = Vulnerable

The scaphoid has a retrograde blood supply. The dorsal scaphoid branch of the radial artery enters the dorsal ridge distally and runs proximally, so the proximal pole is the watershed and the first to die - the same reason proximal pole fractures fail to unite.

MRI Is the Key Test

Plain films can be normal early (Stage I). Diffuse low T1 signal of the scaphoid confirms AVN. MRI also separates complete from partial necrosis (Kalainov), which influences whether a vascularized graft is sensible.

No Guideline - Stage-Based Care

There is no level I evidence and no society guideline. Management is built on small case series: immobilize early disease, graft viable non-arthritic scaphoids, and salvage once the carpus collapses or arthritis appears.

Quick Decision Guide

Herbert-Lanzetta stageImagingPreferred treatmentKey pearl
INormal X-ray, MRI positiveImmobilization, activity change, observeSome viable scaphoids revascularise without surgery
IISclerosis / density change, no fragmentationVascularized bone graft or radial osteotomy (if viable, no arthritis)Best stage for joint-preserving surgery
IIIFragmentation / cystic change of proximal poleGraft if no arthritis; otherwise salvageAssess cartilage and carpal alignment carefully
IVCollapse + peri-scaphoid arthritisSalvage: PRC or four-corner fusionJoint-preserving surgery no longer works
Mnemonic

SCAPHOIDWhy the Scaphoid (and the Proximal Pole) Dies

S
Slender shape
Type 2 slender scaphoid has a sparser intra-osseous vascular network
C
Corticosteroids
Systemic steroids - a recognised AVN risk factor
A
Alcohol / chemotherapy
Cytotoxic drugs and alcohol implicated in case reports
P
Proximal pole watershed
Retrograde supply enters distally - proximal pole is last to perfuse
H
Haematological / connective-tissue disease
SLE, sickle cell, gout, vasculitis
O
Occupational vibration / load
Repetitive impact (e.g. drill operators)
I
Idiopathic core
By definition no acute fracture - true cause often unknown
D
Distal supply only
No proximal nutrient vessel to rescue the proximal pole
S
Slender shape
Type 2 slender scaphoid has a sparser intra-osseous vascular network
P
Proximal pole watershed
Retrograde supply enters distally - proximal pole is last to perfuse
I
Idiopathic core
By definition no acute fracture - true cause often unknown
C
Corticosteroids
Systemic steroids - a recognised AVN risk factor
H
Haematological / connective-tissue disease
SLE, sickle cell, gout, vasculitis
D
Distal supply only
No proximal nutrient vessel to rescue the proximal pole
A
Alcohol / chemotherapy
Cytotoxic drugs and alcohol implicated in case reports
O
Occupational vibration / load
Repetitive impact (e.g. drill operators)

Hook:SCAPHOID spells out both the bone and the reasons its proximal pole is so prone to avascular necrosis.

Mnemonic

SAFCHerbert-Lanzetta Radiographic Stages

S
Stage I - Silent X-ray
Normal radiograph, MRI-only disease
A
Stage II - Altered density
Sclerosis / density change, no fragmentation
F
Stage III - Fragmentation
Cystic change and fragmentation of the proximal pole
C
Stage IV - Collapse + arthritis
Carpal collapse with peri-scaphoid degeneration
S
Stage I - Silent X-ray
Normal radiograph, MRI-only disease
F
Stage III - Fragmentation
Cystic change and fragmentation of the proximal pole
A
Stage II - Altered density
Sclerosis / density change, no fragmentation
C
Stage IV - Collapse + arthritis
Carpal collapse with peri-scaphoid degeneration

Hook:SAFC = Silent, Altered, Fragmented, Collapsed - the radiographic march of an untreated osteonecrotic scaphoid.

Mnemonic

PFESalvage Options Once the Scaphoid Is Gone

P
Proximal row carpectomy
Excise scaphoid, lunate, triquetrum; capitate articulates with radius
F
Four-corner fusion
Excise scaphoid, fuse capitate-hamate-lunate-triquetrum
E
Excision + replacement / fusion
Scaphoid excision (with pyrocarbon/silastic implant historically) or total wrist fusion for end-stage
P
Proximal row carpectomy
Excise scaphoid, lunate, triquetrum; capitate articulates with radius
F
Four-corner fusion
Excise scaphoid, fuse capitate-hamate-lunate-triquetrum
E
Excision + replacement / fusion
Scaphoid excision (with pyrocarbon/silastic implant historically) or total wrist fusion for end-stage

Hook:PFE = the salvage toolkit for an arthritic or collapsed Preiser wrist - motion-preserving (PRC, four-corner) before motion-sacrificing (total fusion).

Overview and Epidemiology

Why Preiser Disease Matters

Preiser disease is rare but a classic exam topic because it forces you to reason from first principles: scaphoid vascular anatomy, the difference between AVN and nonunion, and a staged treatment algorithm where no guideline exists.

Preiser disease is idiopathic avascular necrosis (osteonecrosis) of the scaphoid occurring without an acute fracture. It was first described by Georg Preiser in 1910. The scaphoid is the second most common carpal bone to undergo osteonecrosis after the lunate (Kienbock's disease).

Demographics

  • Age: typically 30-50 years
  • Sex: both sexes affected; several surgical series show a female predominance
  • Laterality: usually unilateral
  • Rarity: only a few hundred cases in the world literature

A pooled literature review of 53 publications captured only around 170 patients in a century.

Natural History

  • Early (I-II): a viable scaphoid may revascularise or remain stable
  • Mid (III): fragmentation and proximal-pole volume loss
  • Advanced (IV): collapse and peri-scaphoid arthritis (SNAC-like pattern)
  • Timeline: months to years

Unlike acute fracture AVN, the necrosis here is primary, not the result of a displaced fragment losing its blood supply.

Preiser Disease vs Scaphoid Nonunion AVN

Both can show proximal-pole sclerosis, but Preiser disease has no fracture line - the necrosis is primary and idiopathic. In nonunion, the AVN is a consequence of a fracture that failed to heal. On MRI, Preiser typically shows necrosis confined to the zone of dead bone, whereas a nonunion shows a discrete fracture line. Getting this distinction right changes both the diagnosis and the operation.

Pathophysiology and Anatomy

Scaphoid Vascular Anatomy

The scaphoid receives roughly 70-80% of its blood (including the entire proximal pole) from the dorsal scaphoid branch of the radial artery, which enters the dorsal ridge distally and runs retrograde toward the proximal pole. The distal pole and tubercle are supplied by volar branches. Because no vessel enters the proximal pole directly, it is the watershed and dies first - the same anatomy that explains delayed union of proximal pole fractures.

Aetiology is multifactorial and, by definition, often unknown:

Risk Factors and Associations

  1. Slender ("type 2") scaphoid morphology

    • A narrow scaphoid has a sparser intra-osseous vascular network
    • Over-represented in operative Preiser series compared with the wider "type 1" scaphoid
  2. Repetitive load and vibration

    • Manual labour, drilling, impact sports
    • Cumulative microtrauma to a marginally perfused bone
  3. Drugs and systemic disease

    • Corticosteroids, cytotoxic chemotherapy, alcohol
    • Systemic lupus erythematosus, vasculitis, sickle cell disease, gout, renal disease
  4. Idiopathic

    • In many patients no cause is ever identified - this is the "core" Preiser group

Pathophysiology cascade:

  1. Compromised perfusion of a marginally vascularised (often slender) scaphoid
  2. Ischaemia of the proximal pole (the watershed zone)
  3. Osteocyte death; dead trabecular bone is not resorbed, producing relative sclerosis on X-ray
  4. Subchondral microfracture and fragmentation
  5. Loss of scaphoid height, carpal malalignment (DISI) and instability
  6. Peri-scaphoid radiocarpal and midcarpal arthritis

Three-Zone MRI Pattern

A radiology study described a three-layered scaphoid in Preiser disease: a proximal zone of osteonecrosis, a middle zone of repair, and a distal zone of viable marrow. Pathological fractures occurred only within the necrotic zone. This maps neatly onto the retrograde, distal-to-proximal blood supply.

Why Sclerosis Appears

Increased density does not mean "more bone". Living bone around the dead segment continues to be remodelled and partly resorbed, while the dead bone is not - so the necrotic area looks relatively dense on radiographs (the same principle as in Kienbock's and femoral head AVN).

Classification Systems

Herbert-Lanzetta Classification (Radiographic)

The original and most widely used staging system, based on plain radiographs and treatment implications.

StageRadiographic findingsScaphoid statusTreatment approach
INormal radiograph; MRI shows AVNStructurally intactImmobilization, observation
IISclerosis / density change, normal shapeIntact, no fragmentationVascularized graft or radial osteotomy
IIIFragmentation / cystic changeProximal pole losing volumeGraft if no arthritis, else salvage
IVCollapse with peri-scaphoid arthritisFragmented, arthritic carpusSalvage (PRC, four-corner fusion)

Stage IV is the prognostic watershed: once peri-scaphoid arthritis is established, joint-preserving surgery is no longer effective and salvage is required.

Kalainov Classification (MRI-based)

Two types based on the extent of necrosis on MRI, which helps decide whether revascularisation makes sense.

TypeMRI findingImplication
Type 1Complete necrosis - the entire scaphoid (proximal and distal) shows AVNWhole bone ischaemic; grafting less likely to rescue it
Type 2Partial necrosis - usually limited to the proximal poleViable distal bone present; better candidate for a vascularized graft

Kalainov's insight was that not all "Preiser" scaphoids are the same: a partially necrotic scaphoid with viable distal bone behaves and responds differently from a wholly dead one.

Schmitt Three-Stage MRI/CT Model

A pathoanatomical staging derived from cross-sectional imaging that mirrors the retrograde blood supply.

  • Initial stage: proximal osteosclerosis with an unaltered scaphoid shape (MRI-only)
  • Advanced stage: pathological fractures and volume loss of the proximal pole
  • Final stage: osteonecrosis of the entire scaphoid

The model emphasises that necrosis begins proximally and that the earliest stage is detectable only on MRI.

Clinical Assessment

History

  • Pain: insidious radial-sided / dorsal wrist pain, worse with activity
  • No significant trauma: or pain disproportionate to a trivial injury
  • Weakness: reduced grip strength
  • Stiffness: progressive loss of wrist motion
  • Risk factors: steroid use, chemotherapy, connective-tissue disease, vibration exposure

A drill operator or manual worker with months of unexplained radial wrist pain is a classic vignette.

Examination

  • Tenderness: over the anatomical snuffbox / scaphoid
  • Swelling: dorsoradial fullness
  • ROM: reduced flexion-extension, painful at extremes
  • Grip: weak and painful
  • Watson (scaphoid shift) test: may be positive if carpal instability has developed

Findings are non-specific; imaging makes the diagnosis.

Differential Diagnosis of Radial Wrist Pain

Radial-sided wrist pain in an adult has several mimics. MRI is the single best discriminator: Preiser disease shows diffuse low T1 marrow signal of the scaphoid without a fracture line, whereas the alternatives below have characteristic alternative patterns.

Differential Diagnosis

ConditionTypical featuresKey imaging discriminatorDistinguishing point from Preiser
Preiser diseaseInsidious radial wrist pain, no acute fractureDiffuse low T1 scaphoid signal, NO fracture linePrimary idiopathic AVN of an intact scaphoid
Scaphoid nonunion (with AVN)Prior wrist injury, snuffbox painDiscrete fracture line plus proximal-pole sclerosisAVN is secondary to a fracture that failed to unite
Occult / acute scaphoid fractureAcute fall on outstretched hand, focal tendernessFracture line on MRI/CT, bone oedemaAcute trauma and a true fracture, not idiopathic AVN
Scapholunate ligament injuryTrauma, dorsal SL tenderness, positive WatsonSL gap (Terry-Thomas), DISI; scaphoid marrow normalLigamentous instability; scaphoid signal is normal
De Quervain tenosynovitisRadial styloid pain, positive FinkelsteinTenosynovitis of first dorsal compartment; bone normalTendon, not bone, pathology
Radioscaphoid (STT) osteoarthritisOlder patient, base-of-thumb / radial painJoint-space loss and osteophytes; no diffuse AVNDegenerative joint disease rather than osteonecrosis

Controversies and Areas of Uncertainty

Unresolved Questions Examiners Probe

Preiser disease has no level I evidence and no consensus guideline. A strong candidate acknowledges the uncertainty rather than overstating any single procedure.

Does it even exist as one entity?

Preiser's original 1910 description was controversial and some early "cases" were probably unrecognised fractures. Modern authors restrict the term to genuinely idiopathic AVN with no fracture, but the boundary with occult fracture and nonunion remains debated.

Surgery vs conservative care

A systematic review found surgery gave greater pain relief than conservative treatment in Stages II-III, but the evidence is entirely Level IV case series. Some early, viable scaphoids revascularise with immobilization alone, so not every patient needs an operation.

Vascularized graft vs salvage

A large single-centre series found pedicled vascularized bone grafts gave functional outcomes similar to salvage procedures but preserved the scaphoid in about 70% of cases - so the trade-off (preserve a partly dead bone vs remove it) is genuinely unsettled.

Can you revascularise the proximal pole?

Even when grafts improve MRI signal, revascularisation of the proximal pole is frequently incomplete, and arthritis can still progress. This tempers enthusiasm for grafting in wholly necrotic (Kalainov type 1) scaphoids.

Role of radial osteotomy

Closing radial wedge osteotomy can relieve pain and preserve motion, but in published series radiographic stage still progressed in many patients - suggesting it is symptom-modifying rather than disease-modifying.

PRC vs four-corner fusion

As in other end-stage carpal collapse, both salvage options give reliable pain relief with broadly comparable function; choice is driven by cartilage status, demand and surgeon preference rather than high-quality comparative data.

Investigations

Investigation Protocol

First LinePlain Radiographs

PA, lateral and scaphoid (ulnar-deviation) views. Look for scaphoid sclerosis (Stage II), fragmentation/cysts (Stage III), collapse and peri-scaphoid arthritis (Stage IV), and any DISI on the lateral. Films are normal in Stage I, so a normal radiograph never excludes the diagnosis.

Key TestMRI

T1 and T2 sequences (consider contrast). Diffuse low T1 signal confirms AVN; absence of a fracture line distinguishes Preiser from nonunion. MRI detects Stage I disease, assesses lunate viability, and separates complete vs partial necrosis (Kalainov) to guide graft suitability.

AdjunctCT Scan

For bony detail and surgical planning. Defines fragmentation, cyst location, collapse and any subtle fracture line. Sagittal-oblique reformats along the scaphoid axis are most useful.

SelectedWrist Arthroscopy

Direct cartilage assessment. Allows grading of articular damage and can be combined with debridement; helps decide between joint-preserving surgery and salvage when imaging is equivocal.

Key Imaging Points

ModalityWhat it showsRole in Preiser disease
RadiographSclerosis, fragmentation, collapse, arthritisHerbert-Lanzetta staging; normal in Stage I
MRIDiffuse low T1 marrow signal, extent of necrosisConfirms diagnosis; Kalainov complete vs partial; detects Stage I
CTTrabecular detail, cysts, fracture line, collapseSurgical planning; excludes occult fracture/nonunion

Management Algorithm

Conservative Management

Indications: Stage I disease, viable scaphoid, low-demand or reluctant patient, significant comorbidity.

Conservative Treatment Steps

First LineImmobilization

Cast or splint for several weeks to months to unload the scaphoid and allow revascularisation. Combine with activity / occupational modification (e.g. moving away from vibration or heavy impact work). Monitor with serial radiographs and MRI.

AdjunctsActivity Modification and Analgesia

Avoid heavy load and vibration. NSAIDs for symptom control. Hand therapy to maintain motion.

SurveillanceSerial Imaging

Repeat MRI to detect revascularisation or progression. Some early, viable scaphoids recover (as in the illustrated case); others progress and need surgery.

Conservative care is most appropriate for genuinely early, viable disease - it is temporizing once fragmentation or arthritis appears.

Joint-Preserving Surgery

Indications: Stage II-III with a viable scaphoid and no radiocarpal arthritis or carpal instability.

Vascularized Bone Graft (VBG)

  • Rationale: deliver living, vascularised bone (commonly a pedicled graft from the distal radius, e.g. 1,2-ICSRA, or the second metacarpal base) into the necrotic scaphoid to restore blood supply
  • Best candidates: early stage, no arthritis, partial (Kalainov type 2) necrosis with viable distal bone
  • Outcomes: reduced pain and preserved motion in most patients; revascularisation of the proximal pole is often incomplete

Radial Osteotomy

  • Closing radial wedge osteotomy can offload the scaphoid and relieve pain while preserving motion
  • Radiographic stage may still progress, so it is largely symptom-modifying

Joint-preserving surgery aims to keep the native scaphoid before collapse and arthritis make this impossible.

Salvage Surgery

Indications: Stage IV (collapse with peri-scaphoid arthritis), failed joint-preserving surgery, wholly necrotic scaphoid.

Proximal Row Carpectomy (PRC)

  • Technique: excise scaphoid, lunate and triquetrum; capitate articulates with the lunate fossa of the radius
  • Requirements: intact capitate head and lunate fossa cartilage
  • Outcomes: reliable pain relief while preserving roughly half of wrist motion

Four-Corner Fusion (with scaphoid excision)

  • Technique: excise scaphoid, fuse capitate-hamate-lunate-triquetrum
  • Outcomes: reliable pain relief, preserves some motion; nonunion and hardware issues are the main risks

Scaphoid Excision / Implant / Total Wrist Fusion

  • Scaphoid excision (historically with silastic or pyrocarbon implants) has a limited, selective role
  • Total wrist fusion for end-stage or failed salvage gives the most reliable pain relief at the cost of all motion

Salvage trades motion for durable pain relief once the joint is destroyed.

Treatment Algorithm by Stage

StagePreferred treatmentAlternativeNotes
IImmobilization + activity changeObservation with serial MRISome viable scaphoids revascularise
IIVascularized bone graftClosing radial wedge osteotomyBest window for joint preservation
IIIVBG if no arthritisSalvage if cartilage damagedDecision hinges on arthritis and necrosis extent
IVPRC or four-corner fusionTotal wrist fusion (end-stage)Joint-preserving surgery no longer effective

Complications

Complications by Treatment

TreatmentEarly complicationsLate complicationsManagement
ConservativePersistent painProgression to collapse / arthritisConvert to surgery
Vascularized graftPedicle injury, stiffnessIncomplete revascularisation, ongoing arthritisSalvage procedure
Radial wedge osteotomyEPL rupture, hardware irritation, DRUJ symptomsStage progression despite pain reliefTendon reconstruction, revision
PRCStiffness, CRPSRadiocapitate arthritis over timeConvert to fusion
Four-corner fusionNonunion, hardware prominenceAdjacent-joint arthritisRevision / total fusion

General Complications

Progression of disease (untreated or after symptom-only surgery):

  • Fragmentation, scaphoid collapse, DISI and peri-scaphoid arthritis
  • Some early viable scaphoids instead revascularise and stabilise

Complex regional pain syndrome (CRPS):

  • Risk after any wrist surgery; minimise with early motion and good analgesia

Stiffness:

  • Common after prolonged immobilization or fusion; early hand therapy mitigates it

Clinical Relevance and Outcomes

Representative Outcomes

TreatmentPain reliefMotionEvidence
Conservative (early, viable)Variable; some full recoveryOften preservedCase reports / small series
Vascularized bone graftImproved in mostPreserved (around half of normal)Level IV series
Radial wedge osteotomyGood pain reliefLargely retainedSmall Level V series
PRC / four-corner fusionReliable pain reliefRoughly 50% of normalLevel IV salvage data

Prognostic factors:

FactorBetter outcomeWorse outcome
Stage at diagnosisI-IIIII-IV
Necrosis extent (Kalainov)Partial (type 2)Complete (type 1)
Cartilage / arthritisIntactPeri-scaphoid arthritis
Carpal alignmentStableDISI / collapse

Bottom line: outcomes are driven by when the disease is caught. Caught early and viable, the scaphoid may be preserved or even revascularise; caught late with collapse and arthritis, salvage gives dependable pain relief but never restores a normal wrist.

Evidence Base

Systematic Literature Review
Bergman, Petit, Rabarin, Raimbeau & Bigorre
Key Findings:
  • Updated review of 53 publications and 170 patients since Preiser's 1910 description
  • Scaphoid is the second most frequent carpal bone for avascular necrosis after the lunate
  • Two modern imaging-based classifications now supplement the original Herbert-Lanzetta radiographic system
  • Proposes a simple staged treatment algorithm given the absence of formal guidelines
Clinical Implication: Preiser disease is rare and poorly standardised; staged, individualised treatment based on radiographs plus MRI is the pragmatic approach.
Source: Hand Surg Rehabil 2021
Verify on PubMed (PMID 33775889)

Imaging Cohort
Schmitt, Frohner, van Schoonhoven, Lanz & Golles
Key Findings:
  • 10 patients with primary scaphoid osteonecrosis imaged with radiographs, CT and contrast-enhanced MRI
  • A three-layered architecture was found: proximal necrosis, middle repair zone, distal viable marrow
  • Pathological fractures occurred exclusively within the necrotic zone, unlike scaphoid nonunion
  • Three morphological stages described; the initial stage is visible only on MRI
Clinical Implication: The retrograde, distal-to-proximal blood supply explains why necrosis starts proximally and why MRI is essential for early diagnosis.
Source: Eur J Radiol 2010
Verify on PubMed (PMID 21112713)

Therapeutic Level IV
Moran, Cooney & Shin
Key Findings:
  • 8 pedicled vascularized bone grafts from the distal radius as primary treatment for Preiser disease
  • All MRIs showed some revascularisation but proximal-pole revascularisation was consistently incomplete
  • Most patients had long-term pain reduction with preserved radiocarpal motion (mean Mayo wrist score 68)
  • Authors recommend VBG only for early disease (Herbert I-II) without arthritis or carpal instability
Clinical Implication: Vascularized bone grafting can relieve pain and preserve the scaphoid in early disease, but cannot reliably revascularise a wholly necrotic proximal pole.
Source: J Hand Surg Am 2006
Verify on PubMed (PMID 16713829)

Therapeutic Level IV
Amundsen, Oh, Huang, Cantwell, Hsu & Moran
Key Findings:
  • 39 wrists (38 patients) operated for Preiser disease over 32 years; mean age 37, median follow-up 5.3 years
  • Pedicled vascular bone grafts gave functional outcomes similar to salvage (four-corner fusion / PRC)
  • Grafting preserved the scaphoid in about 70% of cases; outcomes did not differ by Herbert or Kalainov stage
  • A slender scaphoid shape was more common in the unaffected contralateral wrists of these patients
Clinical Implication: VBG and salvage achieve comparable function, so scaphoid preservation is reasonable in early disease; slender scaphoid morphology may be a predisposing factor.
Source: J Hand Surg Am 2023
Verify on PubMed (PMID 34887136)

Systematic Review (Level IV studies)
Kazemi, Daliri & Moradi
Key Findings:
  • PRISMA review of 42 studies and 135 wrists; all underlying evidence is Level IV case reports/series
  • In Stages II-III, surgery reduced pain more than conservative treatment
  • Vascularized bone grafting was most effective in Stage II without degenerative change
  • Proximal row carpectomy gave the best pain relief and motion in Stage III
Clinical Implication: Stage-matched surgery (VBG for Stage II, PRC for Stage III) outperforms conservative care for pain, but the evidence base is weak.
Source: Orthop Traumatol Surg Res 2022
Verify on PubMed (PMID 36410658)

Therapeutic Level V
Tomori, Sawaizumi, Nanno & Takai
Key Findings:
  • 7 wrists with Preiser disease treated by closing radial wedge osteotomy
  • Wrist pain improved markedly and range of motion / grip strength were largely retained
  • Radiographic disease stage still progressed in 4 of 7 patients despite clinical improvement
  • Complications included one EPL rupture and one case of distal radioulnar joint deterioration
Clinical Implication: Closing radial wedge osteotomy can relieve pain and preserve motion but appears symptom-modifying rather than disease-modifying.
Source: J Hand Surg Am 2019
Verify on PubMed (PMID 30685137)

Therapeutic Level IV
Ishizaka, Moriya, Kuroda, Koda, Tsubokawa & Maki
Key Findings:
  • 9 patients (mostly women) reviewed for the relationship between patient characteristics and treatment choice
  • Most elderly patients presented with advanced-stage disease and concurrent DISI deformity
  • Elderly patients were more often managed non-surgically
  • Where surgery was used, closing radial wedge osteotomy was favoured as the less invasive option
Clinical Implication: Older patients tend to present late with DISI and are often managed conservatively; treatment must be individualised to age, stage and demand.
Source: J Hand Surg Glob Online 2024
Verify on PubMed (PMID 39166199)

Exam Viva Scenarios

Use these scenarios to practise clinical reasoning and management decisions

CLINICAL SCENARIOStandard

Scenario 1: Radial Wrist Pain with a Normal X-ray

CLINICAL PROMPT

"A 36-year-old male drill operator presents with 4 months of insidious radial-sided wrist pain and no clear injury. Snuffbox tenderness is present. Plain radiographs of the wrist are reported as normal. How do you proceed?"

PRACTICAL APPROACH
A normal radiograph does not exclude significant scaphoid pathology. My concern is an occult scaphoid fracture or early scaphoid osteonecrosis - Preiser disease. I would take a focused history for risk factors such as vibration exposure, corticosteroid or chemotherapy use, alcohol and connective-tissue disease, given his occupation as a drill operator. The key investigation is an MRI of the wrist, which will distinguish an occult fracture (a discrete fracture line with surrounding oedema) from Preiser disease (diffuse low T1 marrow signal of the scaphoid without a fracture line). If MRI confirms idiopathic AVN with no fracture, this is Herbert-Lanzetta Stage I disease. I would classify the extent of necrosis on MRI using the Kalainov system - complete versus partial - and assess for any carpal malalignment. For a viable Stage I scaphoid I would begin with immobilization and activity or occupational modification, with serial imaging, because some early viable scaphoids revascularise and stabilise without surgery.
KEY CLINICAL POINTS
Normal X-ray never excludes scaphoid pathology - get an MRI
MRI distinguishes occult fracture (fracture line) from Preiser (diffuse low T1, no fracture line)
Stage I Preiser is MRI-only disease
Kalainov complete vs partial necrosis guides whether grafting is sensible
Early viable scaphoids may revascularise with immobilization and activity change
COMMON PITFALLS
Calling a normal X-ray reassuring and discharging the patient
Forgetting to exclude an occult fracture or nonunion before diagnosing Preiser
Rushing to surgery for early Stage I disease
FURTHER QUESTIONS
"Why is the proximal pole of the scaphoid most affected?"
"How does Preiser disease differ from scaphoid nonunion AVN?"
"What is the Kalainov classification?"
CLINICAL SCENARIOChallenging

Scenario 2: Viable Scaphoid, No Arthritis

CLINICAL PROMPT

"A 40-year-old woman has 8 months of dorsoradial wrist pain. Radiographs show scaphoid sclerosis without fragmentation. MRI confirms avascular necrosis limited to the proximal pole with viable distal bone, and there is no radiocarpal arthritis or carpal instability. What are her options?"

PRACTICAL APPROACH
This is Herbert-Lanzetta Stage II Preiser disease, and on MRI it is a Kalainov partial (proximal-pole) necrosis with viable distal bone - the best scenario for joint-preserving surgery. Because there is no arthritis and no carpal instability, I would offer a vascularized bone graft, typically a pedicled graft from the distal radius such as the 1,2-intercompartmental supraretinacular artery graft, to deliver living bone into the necrotic proximal pole. The evidence is Level IV, but series from Moran and from Mayo show that grafting relieves pain and preserves motion, and preserves the native scaphoid in around 70% of cases with outcomes comparable to salvage. I would counsel her honestly that revascularisation of the proximal pole is frequently incomplete and that arthritis can still progress, so this is not a guaranteed cure. An alternative joint-preserving option is a closing radial wedge osteotomy, which reliably relieves pain but tends to be symptom-modifying rather than disease-modifying. If she later develops collapse and peri-scaphoid arthritis, salvage with proximal row carpectomy or four-corner fusion would be the fallback.
KEY CLINICAL POINTS
Stage II with no arthritis and viable bone = window for joint preservation
Vascularized bone graft (e.g. 1,2-ICSRA from distal radius) is the main option
Grafting preserves the scaphoid in ~70% with outcomes similar to salvage
Counsel that proximal-pole revascularisation is often incomplete
Salvage remains available if disease progresses
COMMON PITFALLS
Offering a vascularized graft when there is already radiocarpal arthritis
Overstating revascularisation - the proximal pole often does not fully recover
Ignoring the option of radial osteotomy or honest non-operative discussion
FURTHER QUESTIONS
"Which vascularized grafts can be used for the scaphoid?"
"When is a graft contraindicated?"
"What does the systematic review evidence actually support?"
CLINICAL SCENARIOCritical

Scenario 3: Collapsed, Arthritic Scaphoid

CLINICAL PROMPT

"A 55-year-old presents late with chronic wrist pain, stiffness and weakness. Radiographs show scaphoid fragmentation and collapse with peri-scaphoid radiocarpal arthritis and a DISI deformity. MRI shows necrosis of the whole scaphoid. How do you manage this, and what does the evidence say?"

PRACTICAL APPROACH
This is Herbert-Lanzetta Stage IV Preiser disease - collapse with established peri-scaphoid arthritis - and on MRI it is a complete (Kalainov type 1) necrosis. Once arthritis and collapse are present, joint-preserving surgery such as vascularized grafting no longer works, so this is a salvage situation. The two motion-preserving options are proximal row carpectomy and scaphoid excision with four-corner fusion. PRC requires intact cartilage on the capitate head and the lunate fossa of the radius, so I would assess those surfaces on CT and, if needed, arthroscopically. If they are intact, PRC is technically simpler with no nonunion risk and gives reliable pain relief with roughly half of wrist motion. If the capitate head is already arthritic, four-corner fusion (excising the scaphoid and fusing capitate-hamate-lunate-triquetrum) is preferable. The systematic review evidence favours PRC for advanced disease in terms of pain relief and motion, though all the data are Level IV. For an elderly, low-demand or failed-salvage patient with global arthritis, total wrist fusion gives the most dependable pain relief at the cost of all motion. I would counsel explicitly on the motion-versus-pain trade-off and that the goal is durable pain relief, not a normal wrist.
KEY CLINICAL POINTS
Stage IV (collapse + arthritis) = salvage, not joint preservation
PRC requires intact capitate head and lunate fossa cartilage
Four-corner fusion if the capitate head is arthritic
Systematic review evidence favours PRC for advanced disease (Level IV)
Total wrist fusion for end-stage / failed salvage
COMMON PITFALLS
Attempting a vascularized graft on a collapsed, arthritic, wholly necrotic scaphoid
Performing PRC without confirming capitate head and radiocarpal cartilage are intact
Failing to counsel on the motion-versus-pain-relief trade-off
FURTHER QUESTIONS
"What are the contraindications to proximal row carpectomy?"
"How do PRC and four-corner fusion compare?"
"When would you choose total wrist fusion?"

MCQ Practice Points

Which Carpal Bone

Q: Which carpal bone is the second most common site of avascular necrosis after the lunate? A: The scaphoid - idiopathic scaphoid osteonecrosis is termed Preiser disease.

Why the Proximal Pole

Q: Why is the proximal pole of the scaphoid most affected in Preiser disease? A: The scaphoid has a retrograde blood supply - the dorsal scaphoid branch of the radial artery enters the dorsal ridge distally and runs proximally, so the proximal pole is the watershed and dies first.

Key Investigation

Q: What is the key investigation for diagnosing early Preiser disease? A: MRI - it detects diffuse low T1 marrow signal (Stage I) before radiographic changes and distinguishes Preiser from scaphoid nonunion by the absence of a fracture line.

Two Classifications

Q: Name the two main classification systems used in Preiser disease. A: The Herbert-Lanzetta radiographic staging (four stages) and the Kalainov MRI classification (complete vs partial necrosis).

When to Graft

Q: When is a vascularized bone graft appropriate in Preiser disease? A: In early disease (Herbert I-II) with a viable scaphoid and no radiocarpal arthritis or carpal instability - ideally a partial (Kalainov type 2) necrosis with viable distal bone.

Salvage of Choice

Q: What is the salvage procedure favoured for advanced (Stage III-IV) Preiser disease in the systematic review evidence? A: Proximal row carpectomy - it gives reliable pain relief and preserves roughly half of wrist motion, provided the capitate head and lunate fossa cartilage are intact.

Guidelines, Registries & Global Practice

Global epidemiology. Preiser disease is rare worldwide - only a few hundred cases exist in the literature, and most hand surgeons see only one or two in a career. It clusters in adults aged 30-50, with several surgical series reporting a female predominance, and is associated with corticosteroids, chemotherapy, alcohol, connective-tissue disease and a slender scaphoid morphology. There is no population incidence figure and no implant registry, because the operations performed (grafts, osteotomies, carpectomies and fusions) are not arthroplasty.

No single global guideline - practice rests on case-series evidence. No society publishes a formal Preiser treatment guideline. Practice converges on a staging-driven algorithm derived from Level IV-V evidence.

How Practice Differs by Setting and School of Thought

Source / settingStaging emphasisEarly disease (Stage I-II)Advanced (III-IV)
North American (ASSH teaching, Mayo series)Herbert-Lanzetta + Kalainov MRIVascularized bone graft for viable, non-arthritic scaphoidsPRC favoured; four-corner fusion if capitate arthritic
European (FESSH / French hand-surgery centres)Herbert-Lanzetta + MRI necrosis extentVascularized graft (Zaidemberg-type) in early stagesScaphoidectomy +/- implant, PRC or carpal arthrodesis
Japanese / Asian centresHerbert-Lanzetta + Kalainov + DISI assessmentClosing radial wedge osteotomy as less-invasive optionConservative care common in elderly; salvage if disabling
Limited-resource settingsPlain radiographs (MRI often unavailable)Immobilization and activity modificationTotal wrist fusion as reliable, low-cost salvage

Registry and high- vs limited-resource practice. Where MRI is freely available, early (Stage I) disease is detected and viable scaphoids can be grafted or simply observed before collapse. Where MRI is scarce, diagnosis is later and total wrist fusion becomes the dependable salvage because it needs no specialist implant and reliably abolishes pain. Vascularized grafting and microsurgical reconstruction are concentrated in specialist hand units.

Consent essentials (universal). For joint-preserving surgery, counsel that proximal-pole revascularisation is often incomplete and arthritis may still progress. For salvage surgery, counsel explicitly on the motion-versus-pain-relief trade-off (PRC and four-corner fusion preserve some motion; total fusion removes motion but most reliably relieves pain), and on progression risk if early disease is managed non-operatively.

PREISER DISEASE

Clinical summary

Key Concepts

  • •Idiopathic AVN of the scaphoid with NO acute fracture
  • •2nd most common carpal AVN after the lunate (Kienbock's)
  • •Proximal pole most affected - retrograde, distally-entering blood supply
  • •Diagnosis of exclusion - rule out occult fracture / nonunion first

Classifications

  • •Herbert-Lanzetta (radiographic): I normal X-ray, II sclerosis, III fragmentation, IV collapse + arthritis
  • •Kalainov (MRI): complete (whole scaphoid) vs partial (proximal pole) necrosis
  • •Schmitt 3-zone model: proximal necrosis, middle repair, distal viable

Investigations

  • •MRI = key test: diffuse low T1, no fracture line; detects Stage I
  • •Radiographs: sclerosis, fragmentation, collapse, arthritis (normal in Stage I)
  • •CT: bony detail, exclude occult fracture, surgical planning

Treatment by Stage

  • •Stage I: immobilization + activity change, serial MRI
  • •Stage II: vascularized bone graft (or radial wedge osteotomy)
  • •Stage III: graft if no arthritis, else salvage
  • •Stage IV: PRC or four-corner fusion; total fusion for end-stage

Exam Pearls

  • •Normal X-ray does NOT exclude Preiser - order an MRI
  • •VBG only for early, viable, non-arthritic scaphoids
  • •Proximal-pole revascularisation after grafting is often incomplete
  • •No level I evidence and no formal guideline - staged, individualised care
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